Familial motor neuron disease Lateral sclerosis:amyotrophic | primary | Progressive:bulbar palsy | spinal muscular atrophy

Progressive bulbar palsy of childhood [Fazio-Londe] Spinal muscular atrophy:adult form | childhood form, type II | distal | juvenile form, type III [Kugelberg-Welander] | scapuloperoneal form

Modifiers The following fourth-character subdivisions are for use with categories E10-E14: Code Title .0 With coma Diabetic:coma with or without ketoacidosis | hyperosmolar coma | hypoglycaemic coma | Hyperglycaemic coma NOS .1 With ketoacidosis Diabetic:acidosis | ketoacidosis | without mention of coma | .2+ With renal complications Diabetic nephropathy (N08.3*) Intracapillary glomerulonephrosis (N08.3*) Kimmelstiel-Wilson syndrome (N08.3*) .3+ With ophthalmic complications Diabetic:cataract (H28.0*) | retinopathy (H36.0*) | .4+ With neurological complications Diabetic:amyotrophy (G73.0*) | autonomic neuropathy (G99.0*) | mononeuropathy ...[+++] (G59.0*) | polyneuropathy (G63.2*) autonomic (G99.0*) | .5 With peripheral circulatory complications Diabetic:gangrene | peripheral angiopathy+ (I79.2*) | ulcer | .6 With other specified complications Diabetic arthropathy+ (M14.2*) Neuropathic diabetic arthropathy+ (M14.6*) .7 With multiple complications .8 With unspecified complications .9 Without complications | Diabetic:coma with or without ketoacidosis | hyperosmolar coma | hypoglycaemic coma | Hyperglycaemic coma NOS | Diabetic:acidosis | ketoacidosis | without mention of coma | Diabetic nephropathy (N08.3*) Intracapillary glomerulonephrosis (N08.3*) Kimmelstiel-Wilson syndrome (N08.3*) | Diabetic:cataract (H28.0*) | retinopathy (H36.0*) | Diabetic:amyotrophy (G73.0*) | autonomic neuropathy (G99.0*) | mononeuropathy (G59.0*) | polyneuropathy (G63.2*) autonomic (G99.0*) | Diabetic:gangrene | peripheral angiopathy+ (I79.2*) | ulcer | Diabetic arthropathy+ (M14.2*) Neuropathic diabetic arthropathy+ (M14.6*)

Disease with characteristics of muscle weakness and atrophy in the lower limbs, most severely affecting the quadriceps. The loss of motor neurons leads to atrophy of the muscles in the lower limbs with manifestations including unsteady walk and walki

Autosomal dominant benign distal spinal muscular atrophy

Distal hereditary motor neuropathy Jerash type

Diaphragmatic spinal muscular atrophy type 2

Syndrome with characteristics of infantile symmetrical distal muscle weakness and atrophy of the lower limbs, bilateral anterior polar cataracts and Dandy-Walker malformation. It has been described in two brothers. No sensorineural or cognitive defic