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Genetics and Prion Diseases
Inherited prion disease
Prion disease
Prion disease associated with AIDS
Sporadic prion disease
Subacute spongiform encephalopathy
Subacute transmissible spongiform encephalopathy
TSE
TSSE
Transmissible spongiform encephalopathy
Transmissible subacute spongiform encephalopathy

Translation of "Inherited prion disease " (English → French) :

inherited prion disease

maladie à prion de forme héréditaire
IATE -
IATE -


prion disease

maladie à prion [ maladie à prions ]
Nervous System | Human Diseases - Various | Animal Diseases
Système nerveux | Maladies humaines diverses | Maladies des animaux


sporadic prion disease

maladie à prions de forme sporadique
IATE -
IATE -


prion disease | transmissible spongiform encephalopathy | TSE [Abbr.]

encéphalopathie spongiforme transmissible | maladie à prions | EST [Abbr.]
IATE - Health | Agricultural activity
IATE - Health | Agricultural activity


Containment Standards for Laboratories, Animal Facilities and Post Mortem Rooms Handling Prion Disease Agents

Normes de confinement pour les laboratoires, les installations vétérinaires et les salles de nécropsie qui manipulent des prions
Titles of Monographs
Titres de monographies


Genetics and Prion Diseases

Génétique et Maladies à prion
Various Proper Names
Appellations diverses


transmissible subacute spongiform encephalopathy | TSSE | transmissible spongiform encephalopathy | TSE | prion disease | subacute transmissible spongiform encephalopathy | subacute spongiform encephalopathy

encéphalopathie spongiforme subaiguë transmissible | ESST | encéphalopathie subaiguë spongiforme transmissible | ESST | encéphalopathie spongiforme transmissible | EST | encéphalopathie spongiforme | maladie à prion | prionose
médecine > sémiologie et pathologie | médecine > neurologie
médecine > sémiologie et pathologie | médecine > neurologie


Prion disease associated with AIDS

maladie à prion associée au SIDA
SNOMEDCT-CA (trouble) / 421009000
SNOMEDCT-CA (trouble) / 421009000


A very rare genetic vascular disease of autosomal recessive inheritance, described in less than 20 patients to date. The disease has manifestations of adult-onset (as early as the second decade of life) isolated calcification of the arteries of the l

syndrome héréditaire de calcification artérielle et articulaire
SNOMEDCT-BE (as early as the second decade of life) isolated calcification of the arteries of the l / 718602007
SNOMEDCT-BE (disorder) / 718602007


A rare inherited mitochondrial disorder due to a defect in mitochondrial protein synthesis. The disease has characteristics of intrauterine growth retardation, metabolic decompensation with recurrent vomiting, persistent severe lactic acidosis, encep

patoencéphalopathie par déficit combiné de la phosphorylation oxydative de type 1
SNOMEDCT-BE (disorder) / 764962002
SNOMEDCT-BE (disorder) / 764962002




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'Inherited prion disease'

Date index:2024-05-17 -

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