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Benign myoclonic epilepsy in infancy
Childhood absence epilepsy
Clonic
Early myoclonic encephalopathy
Epilepsy with myoclonic absences
Impulsive petit mal
Myoclonic
Myoclonic epilepsy
Myoclonic epilepsy in non-progressive encephalopathy
Myoclonic-astatic seizures
Neonatal convulsions
Nonspecific epileptic seizures atonic
Progressive myoclonic epilepsy
Pyknolepsy
Tonic
Tonic-clonic

Translation of "Myoclonic epilepsy " (English → French) :

TERMINOLOGY
see also In-Context Translations below
Benign:myoclonic epilepsy in infancy | neonatal convulsions (familial) | Childhood absence epilepsy [pyknolepsy] Epilepsy with grand mal seizures on awakening Juvenile:absence epilepsy | myoclonic epilepsy [impulsive petit mal] | Nonspecific epileptic seizures:atonic | clonic | myoclonic | tonic | tonic-clonic

Convulsions néonatales bénignes (familiales) Crises non spécifiques:atoniques | cloniques | myocloniques | tonico-cloniques | toniques | Epilepsie (avec):absences de l'adolescence | absences de l'enfance [pyknolepsie] | crises [grand mal] au réveil | myoclonique bénigne de l'enfance | myoclonique [petit mal impulsif] juvénile
WORLD HEALTH ORGANIZATION ICD-10: G40.3
WORLD HEALTH ORGANIZATION ICD-10: G40.3


Myoclonic epilepsy in non-progressive encephalopathy

epilepsie myoclonique des encéphalopathies non-progressives
SNOMEDCT-BE (disorder) / 778047006
SNOMEDCT-BE (disorder) / 778047006


AFG3L2 (AFG3 like matrix AAA peptidase subunit 2) related spastic ataxia, myoclonic epilepsy, neuropathy syndrome

syndrome d'ataxie spastique-epilepsie myoclonique-neuropathie précoce
SNOMEDCT-BE (AFG3 like matrix AAA peptidase subunit 2) related spastic ataxia, myoclonic epilepsy, neuropathy syndrome / 771469002
SNOMEDCT-BE (disorder) / 771469002


Progressive myoclonic epilepsy

épilepsie myoclonique progressive
SNOMEDCT-BE (disorder) / 267581004
SNOMEDCT-BE (disorder) / 267581004


Epilepsy with:myoclonic absences | myoclonic-astatic seizures | Infantile spasms Lennox-Gastaut syndrome Salaam attacks Symptomatic early myoclonic encephalopathy West's syndrome

Encéphalopathie myoclonique précoce symptomatique Epilepsie avec:absences myocloniques | crises astato-myocloniques | Spasmes infantiles Syndrome de:Lennox-Gastaut | West | Tic de Salaam
WORLD HEALTH ORGANIZATION ICD-10: G40.4
WORLD HEALTH ORGANIZATION ICD-10: G40.4


A rare epilepsy syndrome with characteristics of recurrent, long-lasting myoclonic status in infants and young children with a non-progressive encephalopathy, associated with transient and recurring motor, cognitive and/or behavioral disturbances.

epilepsie myoclonique des encéphalopathies non-progressives
SNOMEDCT-CA (trouble) / 778047006
SNOMEDCT-CA (trouble) / 778047006


A cerebral malformation with epilepsy with predominant characteristics of posterior isolated lissencephaly with developmental delay, intellectual disability and epilepsy that usually evolves from West syndrome to Lennox-Gastaut syndrome. Additional f

lissencéphalie par mutation de LIS1
SNOMEDCT-BE (disorder) / 770560008
SNOMEDCT-BE (disorder) / 770560008


Benign childhood epilepsy with centrotemporal EEG spikes Childhood epilepsy with occipital EEG paroxysms

Epilepsie bénigne de l'enfant avec pointes-ondes centro-temporales à l'EEG [Loiseau-Beaussart] Epilepsie de l'enfant avec paroxysmes occipitaux à l'EEG
WORLD HEALTH ORGANIZATION ICD-10: G40.0
WORLD HEALTH ORGANIZATION ICD-10: G40.0


A rare chromosomal anomaly syndrome resulting from a partial interstitial deletion of the short arm of chromosome 9. The disease has characteristics of mild to moderate developmental delay, hand tremors, myoclonic jerks, attention deficit-hyperactivi

syndrome de microdélétion 9p13
SNOMEDCT-BE (disorder) / 764725008
SNOMEDCT-BE (disorder) / 764725008


Early myoclonic encephalopathy

encéphalopathie myoclonique précoce
SNOMEDCT-BE (disorder) / 44423001
SNOMEDCT-BE (disorder) / 44423001
IN-CONTEXT TRANSLATIONS
‘severe myoclonic epilepsy in infancy’ (SMEI), also known as Dravet’s syndrome. This type of epilepsy

d’épilepsie appelée «épilepsie myoclonique sévère du nourrisson» (EMSN), également connue sous le


It is used in conjunction with clobazam and valproate to treat a certain form of epilepsy called severe myoclonic epilepsy in infancy (Dravet’s syndrome), which affects children.

Il est utilisé en association au clobazam et au valproate pour le traitement d’une forme d’épilepsie qui atteint des enfants, appelée épilepsie myoclonique sévère du nourrisson (syndrome de Dravet).


Diacomit is indicated for use in conjunction with clobazam and valproate as adjunctive therapy of refractory generalized tonic-clonic seizures in patients with severe myoclonic epilepsy in infancy (SMEI, Dravet’s syndrome) whose seizures are not adequately controlled with clobazam and valproate.

Diacomit est indiqué en association au valproate de sodium et au clobazam dans le traitement des convulsions tonicocloniques généralisées chez des patients atteints d’une épilepsie myoclonique sévère du nourrisson (EMSN, syndrome de Dravet) et insuffisamment contrôlées par l’association clobazam/valproate de sodium.




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'Myoclonic epilepsy'

Date index:2023-06-02 -

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